Phone:
+1 877 302 8632
Fax:
+1 888 205 9894 (Toll-free)
E-Mail:
orders@antibodies-online.com

TIMM8A/DDP Products

(Translocase of Inner Mitochondrial Membrane 8A (TIMM8A))
This translocase is involved in the import and insertion of hydrophobic membrane proteins from the cytoplasm into the mitochondrial inner membrane. The gene is mutated in Mohr-Tranebjaerg syndrome/Deafness Dystonia Syndrome (MTS/DDS) and it is postulated that MTS/DDS is a mitochondrial disease caused by a defective mitochondrial protein import system. Defects in this gene also cause Jensen syndrome\; an X-linked disease with opticoacoustic nerve atrophy and muscle weakness. This protein, along with TIMM13, forms a 70 kDa heterohexamer. Alternative splicing results in multiple transcript variants encoding distinct isoforms.[provided by RefSeq, Mar 2009].

antibodies-online.com stands for high-quality research products. Search, find and order tools with extensive validation data, images, references. Our scientific customer service is always at your disposal if you have any questions about the selection or application of our products.

Featured TIMM8A/DDP Categories

TIMM8A/DDP Antibodies

High quality antibodies with extensive validation data.

TIMM8A/DDP ELISA Kits

Reliable ELISA kits for a wide range of species.

TIMM8A/DDP Proteins

Proteins for various applications incl. WB, ELISA, IF etc.

Recommended TIMM8A/DDP Antibodies

Product
Reactivity
Application
Validations
Cat. No.
Quantity
Datasheet
Reactivity Human
Application WB, ELISA, IHC (p)
Validations
  • (5)
Cat. No. ABIN560598
Quantity 100 μg
Datasheet Datasheet
Reactivity Human
Application WB, IF
Validations
  • (3)
Cat. No. ABIN514959
Quantity 50 μg
Datasheet Datasheet
Reactivity Human
Application WB, ELISA
Validations
  • (2)
Cat. No. ABIN514961
Quantity 100 μg
Datasheet Datasheet

Recommended TIMM8A/DDP ELISA Kits

Product
Reactivity
Analytical Method
Validations
Cat. No.
Quantity
Datasheet
Reactivity Human
Analytical Method Quantitative Sandwich ELISA
Validations
  • (1)
Cat. No. ABIN6960137
Quantity 96 tests
Datasheet Datasheet
Reactivity Mouse
Analytical Method Quantitative Competition ELISA
Validations
Cat. No. ABIN1745755
Quantity 96 tests
Datasheet Datasheet
Reactivity Rat
Analytical Method Quantitative Competition ELISA
Validations
Cat. No. ABIN1744536
Quantity 96 tests
Datasheet Datasheet

Recommended TIMM8A/DDP Proteins

Product
Reactivity
Source
Validations
Cat. No.
Quantity
Datasheet
Reactivity Human
Source Escherichia coli (E. coli)
Validations
  • (1)
Cat. No. ABIN7125470
Quantity 50 μg
Datasheet Datasheet
Reactivity Human
Source Wheat germ
Validations
  • (1)
Cat. No. ABIN1322778
Quantity 10 μg
Datasheet Datasheet
Reactivity Human
Source Wheat germ
Validations
  • (1)
Cat. No. ABIN1322777
Quantity 25 μg
Datasheet Datasheet

Synonyms and alternative names related to TIMM8A/DDP

translocase of inner mitochondrial membrane 8 homolog A (yeast) (TIMM8A), translocase of inner mitochondrial membrane 8A (TIMM8A), translocase of inner mitochondrial membrane 8A (timm8a), translocase of inner mitochondrial membrane 8 homolog A (yeast) (timm8a), translocase of inner mitochondrial membrane 8 homolog A1 (yeast) (Timm8a1), translocase of inner mitochondrial membrane 8A1 (Timm8a1), ddp, DDP, DDP1, Ddp1, DFN1, DXHXS1274E, Fci-12, im:6896085, MTS, TIM8, tim8a, Tim8a, TIMM8A, timm8a, Timm8a, zgc:100916

Protein level used designations for TIMM8A/DDP

  • translocase of inner mitochondrial membrane 8 homolog A (yeast)
  • mitochondrial import inner membrane translocase subunit Tim8 A
  • Mitochondrial import inner membrane translocase subunit Tim8 A
  • deafness dystonia protein
  • X-linked deafness dystonia protein
  • deafness dystonia protein 1
  • deafness/dystonia peptide
  • deafness dystonia protein 1 homolog
  • translocase of inner mitochondrial membrane 8 homolog a
  • translocase of inner mitochondrial membrane 8 homolog a1
You are here:
Support