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anti-Beaded Filament Structural Protein 1, Filensin (BFSP1) Antibodies

More than 99% of the vertebrate ocular lens is comprised of terminally differentiated lens fiber cells. Additionally we are shipping Filensin Kits (7) and Filensin Proteins (6) and many more products for this protein.

list all antibodies Gene Name GeneID UniProt
BFSP1 631 Q12934
BFSP1 25394 Q02435
BFSP1 12075 A2AMT1
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Top anti-Filensin Antibodies at antibodies-online.com

Showing 10 out of 59 products:

Catalog No. Reactivity Host Conjugate Application Images Quantity Supplier Delivery Price Details
Cow Rabbit Un-conjugated WB WB Suggested Anti-BFSP1 Antibody Titration: 0.2-1 ug/mlPositive Contro... 100 μL Log in to see 2 to 3 Days
$289.00
Details
Human Rabbit Un-conjugated IHC (p), WB 100 μL Log in to see 8 to 10 Days
$507.83
Details
Human Mouse Un-conjugated WB BFSP1 monoclonal antibody (M02), clone 6B4 Western Blot analysis of BF... 0.1 mg Log in to see 8 to 11 Days
$450.00
Details
Human Rabbit Un-conjugated WB 50 μg Log in to see 8 to 10 Days
$551.83
Details
Human Rabbit Un-conjugated ELISA, WB 50 μg Log in to see 2 to 3 Days
$433.13
Details
Human Mouse Un-conjugated IHC (fro), WB   100 μg Log in to see 8 to 10 Days
$449.17
Details
Human Rabbit Un-conjugated WB BFSP1 antibody used at 0.5 ug/ml to detect target protein. 50 μg Log in to see 3 to 4 Days
$510.36
Details
Cow Mouse Un-conjugated IHC (fro), WB   100 μg Log in to see 4 to 6 Days
$200.00
Details
Human Mouse Un-conjugated IP   100 μg Log in to see 8 to 10 Days
$493.17
Details
Human Mouse Un-conjugated WB   100 μL Log in to see 8 to 10 Days
$493.17
Details

BFSP1 Antibodies by Reactivity, Application, Clonality and Conjugate

Attributes Applications Host Clonality
Human , , , ,
,
Rat (Rattus) , , ,

Mouse (Murine) , , ,

Top referenced anti-Filensin Antibodies

  1. Cow (Bovine) Polyclonal Filensin Primary Antibody for WB - ABIN2778759 : Ramachandran, Perumalsamy, Hejtmancik: Autosomal recessive juvenile onset cataract associated with mutation in BFSP1. in Human genetics 2007 (PubMed)

More Antibodies against Filensin Interaction Partners

Human Beaded Filament Structural Protein 1, Filensin (BFSP1) interaction partners

  1. A novel mutation (c.1042G>A) at exon 7 of BFSP1, which creates a substitution of an aspartate to an asparagine (p.D348N) was identified to be associated with autosomal dominant congenital cataract in a Chinese family.

  2. The crystallin beta cluster on chromosome 22, GJA3 (show GJA3 Antibodies), and BFSP1 play a major role in maintaining lens transparency.

  3. This is the first report of a mutation in the BFSP1 gene associated with human inherited cataracts.

Mouse (Murine) Beaded Filament Structural Protein 1, Filensin (BFSP1) interaction partners

  1. disruption of the Hsf4 (show HSF4 Antibodies) gene leads to cataracts via at least three pathways: down-regulation of gamma-crystallin, particularly gamma S-crystallin (show CRYGS Antibodies); decreased lens beaded filament expression; and loss of post-translational modification of alpha A-crystallin (show CRYAA Antibodies)

Filensin (BFSP1) Antigen Profile

Protein Summary

More than 99% of the vertebrate ocular lens is comprised of terminally differentiated lens fiber cells. Two lens-specific intermediate filament-like proteins, CP49 (also known as phakinin) and the protein product of this gene, filensin, are expressed only after fiber cell differentiation has begun. Both proteins are found in a structurally unique cytoskeletal element that is referred to as the beaded filament (BF). Mutations in this gene are the cause of autosomal recessive cortical juvenile-onset cataract. Multiple transcript variants encoding different isoforms have been found for this gene.

Gene names and symbols associated with BFSP1

  • beaded filament structural protein 1, filensin (BFSP1) antibody
  • filensin (Bfsp1) antibody
  • beaded filament structural protein 1, filensin (bfsp1) antibody
  • beaded filament structural protein 1, filensin (LOC100218632) antibody
  • beaded filament structural protein 1, filensin (LOC100220461) antibody
  • beaded filament structural protein 1, filensin (Bfsp1) antibody
  • beaded filament structural protein 1, in lens-CP94 (Bfsp1) antibody
  • filensin-like (LOC100521759) antibody
  • 115-kDa antibody
  • Bfsp1 antibody
  • CP94 antibody
  • CP95 antibody
  • CP97 antibody
  • CP115 antibody
  • CTRCT33 antibody
  • LIFL-H antibody
  • LOC100218632 antibody
  • LOC100220461 antibody
  • MGC84254 antibody

Protein level used designations for BFSP1

beaded filament structural protein 1, filensin , filensin , filensin-like , cytoskeletal protein, 115 KD , lens fiber cell beaded-filament structural protein CP 115 , lens intermediate filament-like heavy , CP97 115-kDa , lens fiber cell beaded-filament structural protein CP 94 , CP95 , lens fiber cell beaded-filament structural protein CP 95 , beaded filament structural protein in lens-CP94

GENE ID SPECIES
695840 Macaca mulatta
458107 Pan troglodytes
100170758 Cavia porcellus
444665 Xenopus laevis
100062535 Equus caballus
100218632 Taeniopygia guttata
100220461 Taeniopygia guttata
100347138 Oryctolagus cuniculus
100392909 Callithrix jacchus
100447671 Pongo abelii
100607956 Nomascus leucogenys
281644 Bos taurus
631 Homo sapiens
101121536 Ovis aries
485756 Canis lupus familiaris
25394 Rattus norvegicus
396056 Gallus gallus
12075 Mus musculus
100521759 Sus scrofa
Selected quality suppliers for anti-Filensin (BFSP1) Antibodies
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