MCCC1 antibody (AA 526-725)

Catalog No. ABIN6143628

Product Details anti-MCCC1 Antibody

Target: MCCC1 (Methylcrotonoyl-CoA Carboxylase 1 (Alpha) (MCCC1))

Binding Specificity: AA 526-725

Reactivity: Human

Host: Rabbit

Clonality: Polyclonal

Conjugate: This MCCC1 antibody is un-conjugated

Application: Western Blotting (WB), Immunohistochemistry (IHC)

Sequence: FTLQAHDQFS PFSSSSGRRL NISYTRNMTL KDGKNNVAIA VTYNHDGSYS MQIEDKTFQV LGNLYSEGDC TYLKCSVNGV ASKAKLIILE NTIYLFSKEG SIEIDIPVPK YLSSVSSQET QGGPLAPMTG TIEKVFVKAG DKVKAGDSLM VMIAMKMEHT IKSPKDGTVK KVFYREGAQA NRHTPLVEFE EEESDKRESE

Cross-Reactivity: Human, Mouse

Characteristics: Polyclonal Antibodies

Immunogen: Recombinant fusion protein containing a sequence corresponding to amino acids 526-725 of human MCCC1 (NP_064551.3).

Isotype: IgG

Application Details

Application Notes: WB,1:500 - 1:1000,IHC,1:50 - 1:100

Restrictions: For Research Use only

Handling

Format: Liquid

Buffer: PBS with 0.02 % sodium azide,50 % glycerol, pH 7.3.

Preservative: Sodium azide

Precaution of Use: This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.

Storage: -20 °C

Storage Comment: Store at -20°C. Avoid freeze / thaw cycles.

Target Details for MCCC1

Target: MCCC1 (Methylcrotonoyl-CoA Carboxylase 1 (Alpha) (MCCC1))

Alternative Name: MCCC1 (MCCC1 Products)

Synonyms: MCC-B antibody, MCCA antibody, 1810045E08Rik antibody, 2310058B18Rik antibody, MCCalpha antibody, Mcca antibody, R75106 antibody, methylcrotonoyl-CoA carboxylase 1 antibody, methylcrotonyl-CoA carboxylase alpha chain antibody, methylcrotonoyl-Coenzyme A carboxylase 1 (alpha) antibody, MCCC1 antibody, Mccc1 antibody, MCCA antibody

Background: This gene encodes the large subunit of 3-methylcrotonyl-CoA carboxylase. This enzyme functions as a heterodimer and catalyzes the carboxylation of 3-methylcrotonyl-CoA to form 3-methylglutaconyl-CoA. Mutations in this gene are associated with 3-Methylcrotonylglycinuria, an autosomal recessive disorder of leucine catabolism.,MCCC1,MCC-B,MCCA,Signal Transduction,Endocrine & Metabolism,Mitochondrial metabolism,Mitochondrial markers,Amino acid metabolism,MCCC1

Molecular Weight: 80 kDa

Gene ID: 56922

UniProt: Q96RQ3