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CEP290 Antibodies

(Centrosomal Protein 290kDa (CEP290))

Explore reliable CEP290 antibodies from a broad selection of renowned manufacturers. Our portfolio enables accurate CEP290 detection across multiple species, including Human, Mouse, Rat, Cow, Horse, and supports diverse research applications such as ELISA, WB, IF (cc), IF (p), IHC.

Quickly find the right antibody using our search, filter, and comparison tools. Each product page provides detailed validation data, literature references, and customer feedback. Unlike comparison-only resources, you can conveniently purchase antibodies directly through our site.

Choose from polyclonal, monoclonal, or recombinant CEP290 antibodies derived from various hosts such as Rabbit, Goat. CEP290, also referred to as CEP290, cep290.L, cep290, Cep290, is a well-characterized target within our validated collection.

Browse our CEP290 antibodies below and order directly to support your research with confidence.

Choose one of 45 CEP290 antibodies from our product listing based on 12 validation images.

45 results :

Verified CEP290 Reactivity: Human ELISA, IHC, IF Host: Goat Polyclonal unconjugated
Catalog No. ABIN334371
 
Verified CEP290 Reactivity: Human ELISA, IHC, ICC Host: Goat Polyclonal unconjugated
Catalog No. ABIN570714
 
CEP290 Reactivity: Human, Mouse ELISA, WB, IF, ICC Host: Rabbit Polyclonal unconjugated
Catalog No. ABIN6257056
 
CEP290 Reactivity: Human WB Host: Rabbit Polyclonal unconjugated
Catalog No. ABIN7266277
 
CEP290 Reactivity: Human, Mouse ELISA, WB Host: Rabbit Polyclonal unconjugated
Catalog No. ABIN3183860
 
CEP290 Reactivity: Human, Mouse ELISA, WB Host: Rabbit Polyclonal unconjugated
Catalog No. ABIN6284993
 
CEP290 Reactivity: Mouse ELISA, IF (cc), IF (p), ICC, IHC (p), IHC (fro) Host: Rabbit Polyclonal unconjugated
Catalog No. ABIN6942529
 
CEP290 Reactivity: Human, Mouse, Rat ELISA, WB, IHC, IF, IP Host: Rabbit Polyclonal unconjugated
Catalog No. ABIN7112607
 
CEP290 Reactivity: Mouse ELISA, IHC (p), IHC (fro) Host: Rabbit Polyclonal Biotin
Catalog No. ABIN6942530
 
CEP290 Reactivity: Mouse IF (cc), IF (p) Host: Rabbit Polyclonal AbBy Fluor® 350
Catalog No. ABIN6942531
 
CEP290 Reactivity: Mouse IF (cc), IF (p) Host: Rabbit Polyclonal AbBy Fluor® 680
Catalog No. ABIN6942536
 
CEP290 Reactivity: Mouse IF (cc), IF (p) Host: Rabbit Polyclonal AbBy Fluor® 488
Catalog No. ABIN6942532
 
CEP290 Reactivity: Mouse IF (cc), IF (p) Host: Rabbit Polyclonal AbBy Fluor® 594
Catalog No. ABIN6942534
 
CEP290 Reactivity: Mouse IF (cc), IF (p) Host: Rabbit Polyclonal AbBy Fluor® 555
Catalog No. ABIN6942533
 
CEP290 Reactivity: Mouse IF (cc), IF (p) Host: Rabbit Polyclonal AbBy Fluor® 750
Catalog No. ABIN6942537
 
CEP290 Reactivity: Mouse IF (cc), IF (p) Host: Rabbit Polyclonal AbBy Fluor® 647
Catalog No. ABIN6942535
 
CEP290 Reactivity: Mouse ELISA, IHC (p), IHC (fro) Host: Rabbit Polyclonal HRP
Catalog No. ABIN6942528
 
CEP290 Reactivity: Mouse IF (cc), IF (p) Host: Rabbit Polyclonal Cy5.5
Catalog No. ABIN6942540
 
CEP290 Reactivity: Mouse IF (cc), IF (p) Host: Rabbit Polyclonal FITC
Catalog No. ABIN6942542
 
CEP290 Reactivity: Mouse IF (cc), IF (p) Host: Rabbit Polyclonal Cy7
Catalog No. ABIN6942541
 
  • Type Primary
    • Primary
  • Application
    • ELISA
    • Western Blotting (WB)
    • Immunofluorescence (Cultured Cells) (IF (cc))
    • Immunofluorescence (Paraffin-embedded Sections) (IF (p))
    • Immunohistochemistry (IHC)
    • Immunofluorescence (IF)
    • Immunohistochemistry (Paraffin-embedded Sections) (IHC (p))
    • Immunocytochemistry (ICC)
    • Immunohistochemistry (Frozen Sections) (IHC (fro))
    • Immunoprecipitation (IP)
    • Immunofluorescence (fixed cells) (IF/ICC)
    • Enzyme Immunoassay (EIA)
  • Reactivity
    • Human
    • Mouse
    • Rat
    • Cow
    • Horse
  • Images available
  • Carrier free only
  • Host
    • Rabbit
    • Goat
  • Clonality
    • Polyclonal
  • Binding Specificity
    • AA 131-230
    • Internal Region
    • AA 86-156
    • AA 2429-2479
    • AA 771-820
    • C-Term
    • AA 1289-1416
    • AA 740-820
    • AA 950-1050
    • Center
    • N-Term
    • Phe812
  • Conjugate
    • Un-conjugated
    • Biotin
    • FITC
    • HRP
    • AbBy Fluor® 350
    • AbBy Fluor® 488
    • AbBy Fluor® 555
    • AbBy Fluor® 594
    • AbBy Fluor® 647
    • AbBy Fluor® 680
    • AbBy Fluor® 750
    • Alexa Fluor 488
    • Alexa Fluor 555
    • Alexa Fluor 594
    • Alexa Fluor 647
    • Alexa Fluor 680
    • Alexa Fluor 750
    • Cy3
    • Cy5
    • Cy5.5
    • Cy7
  • Isotype
    • IgG
  • Format
    • Liquid
  • Grade
    • Verified
  • Supplier
    • antibodies-online
    • Signalway
    • Abbexa
    • Acris
    • Assay Biotechnology Company, Inc.
    • Aviva Systems Biology
    • Cohesion Biosciences
    • Covalab

Latest Publications for our CEP290 Antibodies

Barny, Perrault, Michel, Soussan, Goudin, Rio, Thomas, Attié-Bitach, Hamel, Dollfus, Kaplan, Rozet, Gerard: "Basal exon skipping and nonsense-associated altered splicing allows bypassing complete CEP290 loss-of-function in individuals with unusually mild retinal disease." in: Human molecular genetics, (2018) (PubMed).

Dulla, Aguila, Lane, Jovanovic, Parfitt, Schulkens, Chan, Schmidt, Beumer, Vorthoren, Collin, Garanto, Duijkers, Brugulat-Panes, Semo, Vugler, Biasutto, Adamson, Cheetham: "Splice-Modulating Oligonucleotide QR-110 Restores CEP290 mRNA and Function in Human c.2991+1655A>G LCA10 Models." in: Molecular therapy. Nucleic acids, Vol. 12, pp. 730-740, (2018) (PubMed).

Bangs, Schrode, Hadjantonakis, Anderson: "Lineage specificity of primary cilia in the mouse embryo." in: Nature cell biology, Vol. 17, Issue 2, pp. 113-22, (2015) (PubMed).

Alby, Piquand, Huber, Megarbané, Ichkou, Legendre, Pelluard, Encha-Ravazi, Abi-Tayeh, Bessières, El Chehadeh-Djebbar, Laurent, Faivre, Sztriha, Zombor, Szabó, Failler, Garfa-Traore, Bole, Nitschké et al.: "Mutations in KIAA0586 Cause Lethal Ciliopathies Ranging from a Hydrolethalus Phenotype to Short-Rib Polydactyly Syndrome. ..." in: American journal of human genetics, Vol. 97, Issue 2, pp. 311-8, (2015) (PubMed).

Slaats, Saldivar, Bacal, Zeman, Kile, Hynes, Srivastava, Nazmutdinova, den Ouden, Zagers, Foletto, Verhaar, Miles, Sayer, Cimprich, Giles: "DNA replication stress underlies renal phenotypes in CEP290-associated Joubert syndrome." in: The Journal of clinical investigation, Vol. 125, Issue 9, pp. 3657-66, (2015) (PubMed).

Garanto, van Beersum, Peters, Roepman, Cremers, Collin: "Unexpected CEP290 mRNA splicing in a humanized knock-in mouse model for Leber congenital amaurosis." in: PLoS ONE, Vol. 8, Issue 11, pp. e79369, (2013) (PubMed).

Hopp, Heyer, Hommerding, Henke, Sundsbak, Patel, Patel, Consugar, Czarnecki, Gliem, Torres, Rossetti, Harris: "B9D1 is revealed as a novel Meckel syndrome (MKS) gene by targeted exon-enriched next-generation sequencing and deletion analysis." in: Human molecular genetics, Vol. 20, Issue 13, pp. 2524-34, (2011) (PubMed).

Allocca, Doria, Petrillo, Colella, Garcia-Hoyos, Gibbs, Kim, Maguire, Rex, Di Vicino, Cutillo, Sparrow, Williams, Bennett, Auricchio: "Serotype-dependent packaging of large genes in adeno-associated viral vectors results in effective gene delivery in mice." in: The Journal of clinical investigation, Vol. 118, Issue 5, pp. 1955-64, (2008) (PubMed).

McEwen, Koenekoop, Khanna, Jenkins, Lopez, Swaroop, Martens: "Hypomorphic CEP290/NPHP6 mutations result in anosmia caused by the selective loss of G proteins in cilia of olfactory sensory neurons." in: Proceedings of the National Academy of Sciences of the United States of America, Vol. 104, Issue 40, pp. 15917-22, (2007) (PubMed).

Kurtenbach, Gießl, Strömberg, Kremers, Atorf, Rasche, Neuhaus, Hervé, Brandstätter, Asan, Hatt, Kilimann: "The BEACH Protein LRBA Promotes the Localization of the Heterotrimeric G-protein Golfto Olfactory Cilia." in: Scientific reports, Vol. 7, Issue 1, pp. 8409 (PubMed).

Aliases for CEP290 Antibodies

centrosomal protein 290 (CEP290) Antibodies
centrosomal protein 290 L homeolog (cep290.L) Antibodies
centrosomal protein 290kDa (CEP290) Antibodies
centrosomal protein 290 (cep290) Antibodies
centrosomal protein 290 (Cep290) Antibodies
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