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GATM Products

(Glycine Amidinotransferase (L-Arginine:glycine Amidinotransferase) (GATM))

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This gene encodes a mitochondrial enzyme that belongs to the amidinotransferase family. This enzyme is involved in creatine biosynthesis, whereby it catalyzes the transfer of a guanido group from L-arginine to glycine, resulting in guanidinoacetic acid, the immediate precursor of creatine. Mutations in this gene cause arginine:glycine amidinotransferase deficiency, an inborn error of creatine synthesis characterized by mental retardation, language impairment, and behavioral disorders. [provided by RefSeq, Jul 2008].

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Featured GATM Categories

GATM Antibodies

High quality antibodies with extensive validation data.

GATM ELISA Kits

Reliable ELISA kits for a wide range of species.

GATM Proteins

Proteins for various applications incl. WB, ELISA, IF etc.

Recommended GATM Antibodies

Product
Reactivity
Application
Validations
Cat. No.
Quantity
Datasheet
Reactivity Human, Mouse, Rat
Application WB, IHC, IF
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  • (6)
Cat. No. ABIN7262473
Quantity 200 μL
Datasheet Datasheet

Application WB
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Cat. No. ABIN2783416
Quantity 100 μL
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Reactivity Human
Application WB, IHC, ELISA
Validations
  • (3)
Cat. No. ABIN7154176
Quantity 100 μL
Datasheet Datasheet

Recommended GATM ELISA Kits

Product
Reactivity
Analytical Method
Validations
Cat. No.
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Datasheet
Reactivity Goat
Analytical Method Quantitative
Validations
Cat. No. ABIN993485
Quantity 96 tests
Datasheet Datasheet
Reactivity Pig
Analytical Method Quantitative
Validations
Cat. No. ABIN993486
Quantity 96 tests
Datasheet Datasheet
Reactivity Dog
Analytical Method Quantitative
Validations
Cat. No. ABIN993488
Quantity 96 tests
Datasheet Datasheet

Recommended GATM Proteins

Product
Reactivity
Source
Validations
Cat. No.
Quantity
Datasheet
Reactivity Human
Source Escherichia coli (E. coli)
Validations
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Quantity 50 μg
Datasheet Datasheet
Reactivity Human
Source Wheat germ
Validations
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Cat. No. ABIN1354857
Quantity 10 μg
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Reactivity Human
Source Wheat germ
Validations
  • (1)
Cat. No. ABIN1354859
Quantity 10 μg
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Latest Publications for our GATM products

Köttgen, Glazer, Dehghan, Hwang, Katz, Li, Yang, Gudnason, Launer, Harris, Smith, Arking, Astor, Boerwinkle, Ehret, Ruczinski: "Multiple loci associated with indices of renal function and chronic kidney disease." in: Nature genetics, Vol. 41, Issue 6, pp. 712-7, (2010) (PubMed).

Köttgen, Pattaro, Böger, Fuchsberger, Olden, Glazer, Parsa, Gao, Yang, Smith, OConnell, Li, Schmidt, Tanaka, Isaacs, Ketkar, Hwang, Johnson, Dehghan, Teumer, Paré, Atkinson, Zeller, Lohman et al.: "New loci associated with kidney function and chronic kidney disease...." in: Nature genetics, Vol. 42, Issue 5, pp. 376-84, (2010) (PubMed).

Lion-François, Cheillan, Pitelet, Acquaviva-Bourdain, Bussy, Cotton, Guibaud, Gérard, Rivier, Vianey-Saban, Jakobs, Salomons, des Portes: "High frequency of creatine deficiency syndromes in patients with unexplained mental retardation." in: Neurology, Vol. 67, Issue 9, pp. 1713-4, (2006) (PubMed).

Synonyms and alternative names related to GATM

glycine amidinotransferase (L-arginine:glycine amidinotransferase) L homeolog (gatm.L), glycine amidinotransferase (GATM), glycine amidinotransferase (L-arginine:glycine amidinotransferase) (Gatm), glycine amidinotransferase (Gatm), glycine amidinotransferase (L-arginine:glycine amidinotransferase) (gatm), 1810003P21Rik, AGAT, AI314789, AT, cb409, CCDS3, wu:fa08a06, zgc:65855

Protein level used designations for GATM

  • L-arginine:glycine amidinotransferase
  • Transamidinase
  • glycine amidinotransferase, mitochondrial
  • arginine:glycine amidinotransferase
  • transamidinase
  • AT
  • L-arginine: glycine amidinotransferase
  • l-arginine:glycine amidinotransferase
  • agat
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