Glycine Cleavage System H Protein Proteins (GCSH)

Degradation of glycine is brought about by the glycine cleavage system, which is composed of four mitochondrial protein components: P protein (a pyridoxal phosphate-dependent glycine decarboxylase), H protein (a lipoic acid-containing protein), T protein (a tetrahydrofolate-requiring enzyme), and L protein (a lipoamide dehydrogenase). Additionally we are shipping Glycine Cleavage System H Protein Antibodies (57) and Glycine Cleavage System H Protein Kits (5) and many more products for this protein.

list all proteins Gene Name GeneID UniProt
GCSH 2653 P23434
GCSH 171133 Q5I0P2
GCSH 68133 Q91WK5
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Top Glycine Cleavage System H Protein Proteins at antibodies-online.com

Showing 10 out of 10 products:

Catalog No. Origin Source Conjugate Images Quantity Supplier Delivery Price Details
Escherichia coli (E. coli) Human His tag „Crystallography Grade“ protein due to multi-step, protein-specific purification process 1 mg Log in to see 30 to 35 Days
$4,331.68
Details
Escherichia coli (E. coli) Mouse His tag „Crystallography Grade“ protein due to multi-step, protein-specific purification process 1 mg Log in to see 30 to 35 Days
$4,331.68
Details
Escherichia coli (E. coli) Human His tag 100 μg Log in to see 15 to 19 Days
$319.00
Details
Yeast Cow His tag   1 mg Log in to see 60 to 71 Days
$2,253.17
Details
HEK-293 Cells Human Myc-DYKDDDDK Tag Validation with Western Blot 20 μg Log in to see 10 to 12 Days
$785.40
Details
Wheat germ Human GST tag 10 μg Log in to see 11 to 12 Days
$405.71
Details
Escherichia coli (E. coli) Human His tag 100 μg Log in to see 20 to 21 Days
$437.80
Details
Yeast Rat His tag   1 mg Log in to see 60 to 71 Days
$2,253.17
Details
Yeast Chicken His tag   1 mg Log in to see 60 to 71 Days
$2,253.17
Details
Yeast Rabbit His tag   1 mg Log in to see 60 to 71 Days
$2,253.17
Details

GCSH Proteins by Origin and Source

Origin Expressed in Conjugate
Human , ,
, ,
Rat (Rattus)

Mouse (Murine)

More Proteins for Glycine Cleavage System H Protein (GCSH) Interaction Partners

Human Glycine Cleavage System H Protein (GCSH) interaction partners

  1. Data indicate no mutation was found in glycine cleavage system protein-H (GCSH) and suggest that mutations in both glycine decarboxylase (GLDC (show GLDC Proteins)) and aminomethyltransferase (AMT (show AMT Proteins)) are the main cause of glycine encephalopathy in Malaysian population.

  2. Heterozygous GCSH gene mutation in transient neonatal hyperglycinemia.

  3. Genetic analysis showed a non-previously described mutation affecting a consensus splice site (IVS2-1G > C 3) in the AMT (show AMT Proteins) gene encoding the T protein of the glycine cleavage system.

Cow (Bovine) Glycine Cleavage System H Protein (GCSH) interaction partners

  1. X-ray crystal structure of bovine H-protein (show MYBPH Proteins), a component of the glycine cleavage system, was determined at 0.88 A resolution.

Glycine Cleavage System H Protein (GCSH) Protein Profile

Protein Summary

Degradation of glycine is brought about by the glycine cleavage system, which is composed of four mitochondrial protein components: P protein (a pyridoxal phosphate-dependent glycine decarboxylase), H protein (a lipoic acid-containing protein), T protein (a tetrahydrofolate-requiring enzyme), and L protein (a lipoamide dehydrogenase). The protein encoded by this gene is the H protein, which transfers the methylamine group of glycine from the P protein to the T protein. Defects in this gene are a cause of nonketotic hyperglycinemia (NKH). Two transcript variants, one protein-coding and the other probably not protein-coding,have been found for this gene. Also, several transcribed and non-transcribed pseudogenes of this gene exist throughout the genome.

Gene names and symbols associated with GCSH

  • glycine cleavage system protein H (GCSH)
  • glycine cleavage system protein H (aminomethyl carrier) pseudogene (LOC100138886)
  • glycine cleavage system H protein, mitochondrial (LOC742399)
  • glycine cleavage system protein H (aminomethyl carrier) (GCSH)
  • glycine cleavage system protein H (aminomethyl carrier) pseudogene (LOC508238)
  • glycine cleavage system protein H (Gcsh)
  • glycine cleavage system protein H (aminomethyl carrier) (Gcsh)
  • glycine cleavage system lipoyl carrier protein GcvH (gcvH-2)
  • glycine cleavage system H protein (gcvH)
  • glycine cleavage system protein H (aminomethyl carrier), a (gcsha)
  • glycine cleavage system protein H (gcvH)
  • glycine cleavage system carrier of aminomethyl moiety GcvH (gcvH)
  • leucine rich repeat containing 34 (LRRC34)
  • glycine cleavage system protein H (aminomethyl carrier) L homeolog (gcsh.L)
  • 1100001L02Rik protein
  • 5730591C18Rik protein
  • BA5228 protein
  • gce protein
  • gcsh protein
  • H-PROTEIN protein
  • nkh protein
  • wu:fb14d10 protein
  • wu:fw84b08 protein
  • zgc:112535 protein

Protein level used designations for GCSH

glycine cleavage system H protein, mitochondrial , lipoic acid-containing protein , mitochondrial glycine cleavage system H-protein , glycine cleavage system protein H (aminomethyl carrier) , H protein , hydrogen carrier protein , glycine cleavage system H protein , glycine cleavage system protein H , glycine cleavage system protein H (aminomethyl carrier) L homeolog

GENE ID SPECIES
2653 Homo sapiens
100138886 Bos taurus
317723 Bos taurus
468042 Pan troglodytes
742399 Pan troglodytes
479633 Canis lupus familiaris
100009476 Oryctolagus cuniculus
508238 Bos taurus
171133 Rattus norvegicus
415803 Gallus gallus
68133 Mus musculus
2688047 Geobacter sulfurreducens PCA
3727553 Carboxydothermus hydrogenoformans Z-2901
541329 Danio rerio
1084664 Bacillus anthracis str. Ames
1168635 Shewanella oneidensis MR-1
1209626 Coxiella burnetii RSA 493
2799475 Listeria monocytogenes serotype 4b str. F2365
512714 Bos taurus
100721850 Cavia porcellus
447492 Xenopus laevis
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