136 kDa double-stranded RNA-binding protein,136 kDa double stranded RNA binding protein,Adar 1,ADAR,Adar1,Adenosine deaminase acting on RNA 1 A,Adenosine deaminase RNA specific 1,Adenosine deaminase RNA specific,Adenosine deaminase that act on RNA,AGS6,AV242451,Double stranded RNA specific adenosine deaminase,Double-stranded RNA-specific adenosine deaminase,Double-stranded RNA-specific editase Adar,DRADA,Dsh,Dsrad,DSRAD,dsRNA adenosine deaminase,EC 3.5.4.-,G1P1,IFI 4,IFI-4,IFI4,Ifi4 protein,Interferon induced protein 4,Interferon inducible protein 4,Interferon-inducible protein 4,K88DSRBP,mZaADAR,P136,Pre-mRNA adenosine deaminase,RNA adenosine deaminase 1,RNA-editing deaminase 1,RNA-editing enzyme 1,This gene encodes the enzyme responsible for RNA editing by site-specific deamination of adenosines. This enzyme destabilizes double-stranded RNA through conversion of adenosine to inosine. Mutations in this gene have been associated with dyschromatosis symmetrica hereditaria. Alternative splicing results in multiple transcript variants.