Medium-Chain Specific Acyl-CoA Dehydrogenase, Mitochondrial antibody

Catalog No. ABIN5965186

Product Details

Target: Medium-Chain Specific Acyl-CoA Dehydrogenase, Mitochondrial

Reactivity: Human, Mouse, Rat

Host: Rabbit

Clonality: Polyclonal

Conjugate: Un-conjugated

Application: Immunofluorescence (IF)

Purification: Affinity purification

Immunogen: Recombinant fusion protein of human ACADM (NP_000007.1).

Isotype: IgG

Application Details

Application Notes: IF 1:50-1:200

Restrictions: For Research Use only

Handling

Format: Liquid

Concentration: 1 mg/mL

Buffer: PBS with 0.02 % sodium azide, 50 % glycerol, pH 7.3

Preservative: Sodium azide

Precaution of Use: This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.

Storage: -20 °C

Storage Comment: Store at -20°C. Avoid freeze / thaw cycles.

Target Details

Target: Medium-Chain Specific Acyl-CoA Dehydrogenase, Mitochondrial

Alternative Name: ACADM

Synonyms: ACAD1 antibody, MCAD antibody, MCADH antibody, AU018656 antibody, acyl-CoA dehydrogenase medium chain antibody, acyl-Coenzyme A dehydrogenase, medium chain antibody, acyl-CoA dehydrogenase, C-4 to C-12 straight chain antibody, ACADM antibody, Acadm antibody

Background: This gene encodes the medium-chain specific (C4 to C12 straight chain) acyl-Coenzyme A dehydrogenase. The homotetramer enzyme catalyzes the initial step of the mitochondrial fatty acid beta-oxidation pathway. Defects in this gene cause medium-chain acyl-CoA dehydrogenase deficiency, a disease characterized by hepatic dysfunction, fasting hypoglycemia, and encephalopathy, which can result in infantile death. Alternatively spliced transcript variants encoding different isoforms have been found for this gene.

Molecular Weight:

Observed_MW: 47kDa

Calculated_MW: 46kDa/47kDa

Gene ID: 34

UniProt: P11310