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BCKDHB antibody (AA 183-392)
BCKDHB
Reactivity: Human
WB
Host: Rabbit
Polyclonal
unconjugated
Product Details anti-BCKDHB Antibody
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Target
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BCKDHB
(Branched Chain Keto Acid Dehydrogenase E1, beta Polypeptide (BCKDHB))
Binding Specificity
All epitopes for BCKDHB antibodies
AA 183-392
Reactivity
All reactivities for BCKDHB antibodies
Human
Host
All hosts for BCKDHB antibodies
Rabbit
Clonality
All clonalities for BCKDHB antibodies
Polyclonal
Conjugate
All conjugates for BCKDHB antibodies
This BCKDHB antibody is un-conjugated
Application
All applications for BCKDHB antibodies
Western Blotting (WB)
Sequence
RSPWGCVGHG ALYHSQSPEA FFAHCPGIKV VIPRSPFQAK GLLLSCIEDK NPCIFFEPKI LYRAAAEEVP IEPYNIPLSQ AEVIQEGSDV TLVAWGTQVH VIREVASMAK EKLGVSCEVI DLRTIIPWDV DTICKSVIKT GRLLISHEAP LTGGFASEIS STVQEECFLN LEAPISRVCG YDTPFPHIFE PFYIPDKWKC YDALRKMINY
Cross-Reactivity
Mouse
Characteristics
Polyclonal Antibodies
Purification
Affinity purification
Immunogen
Recombinant fusion protein containing a sequence corresponding to amino acids 183-392 of human BCKDHB (NP_898871.1).
Isotype
IgG
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Alternatives
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Application Details
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Application Notes
WB,1:500 - 1:2000
Restrictions
For Research Use only
Handling
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Format
Liquid
Buffer
PBS with 0.02 % sodium azide,50 % glycerol, pH 7.3.
Preservative
Sodium azide
Precaution of Use
This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
Storage
-20 °C
Storage Comment
Store at -20°C. Avoid freeze / thaw cycles.
Target Details for BCKDHB
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Target
BCKDHB
(Branched Chain Keto Acid Dehydrogenase E1, beta Polypeptide (BCKDHB))
Alternative Name
BCKDHB (BCKDHB Products )
Synonyms
zgc:158777 antibody, BCKDHB antibody, E1B antibody, dJ279A18.1 antibody, branched chain keto acid dehydrogenase E1, beta polypeptide antibody, branched chain keto acid dehydrogenase E1 subunit beta antibody, branched chain keto acid dehydrogenase E1, beta polypeptide S homeolog antibody, branched chain ketoacid dehydrogenase E1, beta polypeptide antibody, BCKDHB antibody, bckdhb antibody, bckdhb.S antibody, Bckdhb antibody
Background
This gene encodes the E1 beta subunit of branched-chain keto acid dehydrogenase, which is a multienzyme complex associated with the inner membrane of mitochondria. This enzyme complex functions in the catabolism of branched-chain amino acids. Mutations in this gene have been associated with maple syrup urine disease (MSUD), type 1B, a disease characterized by a maple syrup odor to the urine in addition to mental and physical retardation and feeding problems. Alternative splicing at this locus results in multiple transcript variants.,BCKDHB,BCKDE1B,BCKDH E1-beta,E1B,BCKDHE1-beta,Cancer,Signal Transduction,Endocrine & Metabolism,Mitochondrial metabolism,Mitochondrial markers,Amino acid metabolism,BCKDHB
Molecular Weight
23 kDa/43 kDa
Gene ID
594
UniProt
P21953
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