FH antibody (AA 411-510) (Alexa Fluor 488)

Catalog No. ABIN897948

Product Details anti-FH Antibody (Alexa Fluor 488)

Target: FH (Fumarate Hydratase (FH))

Binding Specificity: AA 411-510

Reactivity: Human

Host: Rabbit

Clonality: Polyclonal

Conjugate: This FH antibody is conjugated to Alexa Fluor 488

Application: Immunofluorescence (Paraffin-embedded Sections) (IF (p)), Immunofluorescence (Cultured Cells) (IF (cc))

Predicted Reactivity: Human,Mouse,Rat,Dog,Cow,Sheep,Pig,Horse,Rabbit

Purification: Purified by Protein A.

Immunogen: KLH conjugated synthetic peptide derived from human Fumarate hydratase (447-496aa)

Isotype: IgG

Application Details

Application Notes: IF(IHC-P) 1:50-200
IF(IHC-F) 1:50-200
IF(ICC) 1:50-200

Restrictions: For Research Use only

Handling

Format: Liquid

Concentration: 1 μg/μL

Buffer: Aqueous buffered solution containing 0.01M TBS ( pH 7.4) with 1 % BSA, 0.03 % Proclin300 and 50 % Glycerol.

Preservative: ProClin

Precaution of Use: This product contains ProClin: a POISONOUS AND HAZARDOUS SUBSTANCE, which should be handled by trained staff only.

Storage: -20 °C

Storage Comment: Store at -20°C. Aliquot into multiple vials to avoid repeated freeze-thaw cycles.

Expiry Date: 12 months

Target Details for FH

Target: FH (Fumarate Hydratase (FH))

Alternative Name: Fumarate hydratase/FH (FH Products)

Synonyms: FH antibody, DDBDRAFT_0205237 antibody, DDBDRAFT_0231397 antibody, DDBDRAFT_0231400 antibody, DDB_0205237 antibody, DDB_0231397 antibody, DDB_0231400 antibody, HLRCC antibody, LRCC antibody, MCL antibody, MCUL1 antibody, Fh1 antibody, im:7152785 antibody, ns:zf-e152 antibody, zf-e152 antibody, zgc:66253 antibody, zgc:77498 antibody, Fh antibody, Fh-1 antibody, fumarate hydratase antibody, fumarate hydratase 1 antibody, FH antibody, fumH antibody, Fh antibody, fh antibody, Fh1 antibody

Background:

Synonyms: mitochondrial, FH, Fumarase, Fumarate hydratase, Fumarate hydratase mitochondrial, FUMH_HUMAN, HLRCC, LRCC, MCL, MCUL 1, MCUL1, Multiple hereditary cutaneous leiomyomata.

Background: Defects in FH are the cause of fumarase deficiency (FHD)also known as fumaricaciduria. FHD is characterized by progressive encephalopathy, developmental delay, hypotonia, cerebral atrophy and lactic and pyruvic acidemia.

Gene ID: 2271