BSCL2 antibody (Berardinelli-Seip Congenital Lipodystrophy 2 (Seipin)) (C-Term)

Details for Product anti-BSCL2 Antibody No. ABIN928313
Antigen
Epitope
C-Term
9
9
8
3
2
2
2
1
1
1
1
Reactivity
Human
32
3
3
2
2
2
1
1
1
Host
Rabbit
26
6
1
Clonality
Polyclonal
Conjugate
This BSCL2 antibody is un-conjugated
2
2
2
2
2
2
Application
Western Blotting (WB)
33
22
19
2
1
1
Options
Immunogen BSCL2 antibody was raised in rabbit using the C terminal of BSCL2 as the immunogen
Purification Purified
Antigen
Alternative Name BSCL2 (BSCL2 Antibody Abstract)
Background This gene encodes protein seipin, which is located in the endoplasmic reticulum and may be important for lipid droplet morphology. Mutations in this gene have been associated with congenital generalized lipodystrophy type 2 or Berardinelli-Seip syndrome, a rare autosomal recessive disease characterized by a near absence of adipose tissue and severe insulin resistance. Alternatively spliced transcript variants encoding different isoforms have been found for this gene. Synonyms: Polyclonal BSCL2 antibody, Anti-BSCL2 antibody, Berardinelli-Seip congenital lipodystrophy 2, seipin antibody, GNG3LG antibody, HMN5 antibody, MGC4694 antibody, SPG17 antibody.
Application Notes WB: 0.2-1 µg/mL
Optimal conditions should be determined by the investigator.
Comment

BSCL2 Blocking Peptide, catalog no. 33R-7521, is also available for use as a blocking control in assays to test for specificity of this BSCL2 antibody

Restrictions For Research Use only
Format Lyophilized
Concentration Lot specific
Buffer Lyophilized powder. Add 50 µL of distilled water. Final antibody concentration is 1 mg/mL in PBS buffer.
Handling Advice Avoid repeated freeze/thaw cycles.
Storage RT/-20 °C
Storage Comment Store at 4 °C, following reconstitution, aliquot and store at -20 °C.
Supplier Images
Image no. 1 for anti-Berardinelli-Seip Congenital Lipodystrophy 2 (Seipin) (BSCL2) (C-Term) antibody (ABIN928313) Western Blot showing BSCL2 antibody used at a concentration of 1-2 ug/ml to detect it...