EPM2A antibody (AA 101-199)
EPM2A
Reactivity: Human
WB, ELISA
Host: Mouse
Monoclonal
4A12
unconjugated
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Target
See all EPM2A Antibodies
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EPM2A
(Epilepsy, Progressive Myoclonus Type 2A, Lafora Disease (Laforin) (EPM2A))
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Binding Specificity
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AA 101-199
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Reactivity
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Human
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Host
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Mouse
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Clonality
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Monoclonal
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Conjugate
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This EPM2A antibody is un-conjugated
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Application
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Western Blotting (WB), ELISA
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Purpose
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Mouse monoclonal antibody raised against a partial recombinant EPM2A.
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Sequence
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GNGPHHDRCC TYNENNLVDG VYCLPIGHWI EATGHTNEMK HTTDFYFNIA GHQAMHYSRI LPNIWLGSCP RQVEHVTIKL KHELGITAVM NFQTEWDIV
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Cross-Reactivity
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Human, Rat
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Characteristics
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Antibody Reactive Against Recombinant Protein.
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Immunogen
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EPM2A (NP_001018051, 101 a.a. ~ 199 a.a) partial recombinant protein with GST tag. MW of the GST tag alone is 26 KDa.
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Clone
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4A12
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Isotype
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IgG2a
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Top Product
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Discover our top product EPM2A Primary Antibody
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Application Notes
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Optimal working dilution should be determined by the investigator.
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Restrictions
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For Research Use only
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Buffer
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In 1x PBS, pH 7.4
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Handling Advice
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Aliquot to avoid repeated freezing and thawing.
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Storage
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-20 °C
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Storage Comment
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Store at -20°C or lower. Aliquot to avoid repeated freezing and thawing.
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Sherwood, Johnson, Delgado-Escueta, Gentry: "A bioassay for Lafora disease and laforin glucan phosphatase activity." in: Clinical biochemistry, Vol. 46, Issue 18, pp. 1869-76, (2013) (PubMed).
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Target
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EPM2A
(Epilepsy, Progressive Myoclonus Type 2A, Lafora Disease (Laforin) (EPM2A))
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Alternative Name
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EPM2A (EPM2A Products)
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Synonyms
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TG-B antibody, Tg(TcraK,TcrbK)TG-BFlv antibody, EPM2 antibody, MELF antibody, laforin antibody, EPM2A, laforin glucan phosphatase antibody, epilepsy, progressive myoclonic epilepsy, type 2 gene alpha antibody, EPM2A antibody, Epm2a antibody
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Background
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Full Gene Name: epilepsy, progressive myoclonus type 2A, Lafora disease (laforin)
Synonyms: EPM2,MELF
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Gene ID
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7957
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NCBI Accession
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NM_001018041
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Pathways
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Cellular Glucan Metabolic Process
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