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TTR antibody
TTR
Reactivity: Human
WB, IHC (p)
Host: Mouse
Monoclonal
2B12
unconjugated
Product Details anti-TTR Antibody
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Target
See all TTR Antibodies
TTR
(Transthyretin (TTR))
Reactivity
All reactivities for TTR antibodies
Human
Host
All hosts for TTR antibodies
Mouse
Clonality
All clonalities for TTR antibodies
Monoclonal
Conjugate
All conjugates for TTR antibodies
This TTR antibody is un-conjugated
Application
All applications for TTR antibodies
Western Blotting (WB), Immunohistochemistry (Paraffin-embedded Sections) (IHC (p))
Specificity
Amyloid polyneuropathy,Amyloidosis I,ATTR,Carpal tunnel syndrome 1,CTS,CTS1,Dysprealbuminemic euthyroidal hyperthyroxinemia,Dystransthyretinemic hyperthyroxinemia,Epididymis luminal protein 111,HEL111,HsT2651,PALB,Prealbumin amyloidosis type I,Prealbumin,Prealbumin Thyroxine-binding,Senile systemic amyloidosis,TBPA,Thyroxine binding prealbumin,Transthyretin,TTHY,TTR,TTR protein
Purification
Protein A purification
Immunogen
Recombinant Protein of TTR
Clone
2B12
Isotype
IgG
Top Product
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Alternatives
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Application Details
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Application Notes
WB 1:500-2000, IHC 1:50-300
Restrictions
For Research Use only
Handling
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Format
Liquid
Concentration
1 mg/mL
Buffer
PBS with 0.02 % sodium azide and 50 % glycerol pH 7.4.
Preservative
Sodium azide
Precaution of Use
This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
Storage
-20 °C
Storage Comment
Store at -20°C. Avoid freeze / thaw cycles.
Target Details for TTR
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Target
TTR
(Transthyretin (TTR))
Alternative Name
TTR (TTR Products )
Synonyms
zgc:103583 antibody, TTR antibody, LOC100226992 antibody, CTS antibody, CTS1 antibody, HsT2651 antibody, PALB antibody, TBPA antibody, AA408768 antibody, AI787086 antibody, D17860 antibody, prealbumin antibody, Lr1 antibody, Tbpa antibody, Prealbumin antibody, xTTR antibody, transthyretin (prealbumin, amyloidosis type I) antibody, transthyretin antibody, Transthyretin antibody, transthyretin (prealbumin, amyloidosis type 1) antibody, transthyretin-like antibody, transthyretin L homeolog antibody, ttr antibody, TTR antibody, vpb38 antibody, MRAD2831_RS38185 antibody, Caci_4246 antibody, LOC100226992 antibody, Ttr antibody, ttr.L antibody
Background
This gene encodes transthyretin, one of the three prealbumins including alpha-1-antitrypsin, transthyretin and orosomucoid. Transthyretin is a carrier protein, it transports thyroid hormones in the plasma and cerebrospinal fluid, and also transports retinol (vitamin A) in the plasma. The protein consists of a tetramer of identical subunits. More than 80 different mutations in this gene have been reported, most mutations are related to amyloid deposition, affecting predominantly peripheral nerve and/or the heart, and a small portion of the gene mutations is non-amyloidogenic. The diseases caused by mutations include amyloidotic polyneuropathy, euthyroid hyperthyroxinaemia, amyloidotic vitreous opacities, cardiomyopathy, oculoleptomeningeal amyloidosis, meningocerebrovascular amyloidosis, carpal tunnel syndrome, etc.
Gene ID
7276
UniProt
P02766
Pathways
Hormone Transport
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