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CLCN1 Products

(Chloride Channel 1, Skeletal Muscle (CLCN1))
The CLCN family of voltage-dependent chloride channel genes comprises nine members (CLCN1-7, Ka and Kb) which demonstrate quite diverse functional characteristics while sharing significant sequence homology. The protein encoded by this gene regulates the electric excitability of the skeletal muscle membrane. Mutations in this gene cause two forms of inherited human muscle disorders: recessive generalized myotonia congenita (Becker) and dominant myotonia (Thomsen). Alternative splicing results in multiple transcript variants. [provided by RefSeq, Mar 2012].

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Featured CLCN1 Categories

CLCN1 Antibodies

High quality antibodies with extensive validation data.

CLCN1 ELISA Kits

Reliable ELISA kits for a wide range of species.

CLCN1 Proteins

Proteins for various applications incl. WB, ELISA, IF etc.

Recommended CLCN1 Antibodies

Product
Reactivity
Application
Validations
Cat. No.
Quantity
Datasheet
Reactivity Human
Application WB, IHC
Validations
  • (3)
Cat. No. ABIN6138661
Quantity 100 μL
Datasheet Datasheet
Reactivity Human, Mouse
Application WB, FACS
Validations
  • (2)
Cat. No. ABIN6243383
Quantity 200 μL
Datasheet Datasheet
Reactivity Human
Application ELISA, IF
Validations
  • (1)
Cat. No. ABIN7147573
Quantity 100 μg
Datasheet Datasheet

Recommended CLCN1 ELISA Kits

Product
Reactivity
Analytical Method
Validations
Cat. No.
Quantity
Datasheet
Reactivity Mouse
Analytical Method Quantitative
Validations
Cat. No. ABIN512658
Quantity 96 tests
Datasheet Datasheet
Reactivity Cow
Analytical Method Quantitative
Validations
Cat. No. ABIN1052024
Quantity 96 tests
Datasheet Datasheet
Reactivity Dog
Analytical Method Quantitative
Validations
Cat. No. ABIN1052025
Quantity 96 tests
Datasheet Datasheet

Recommended CLCN1 Proteins

Product
Reactivity
Source
Validations
Cat. No.
Quantity
Datasheet
Reactivity Human
Source Wheat germ
Validations
  • (1)
Cat. No. ABIN1349563
Quantity 25 μg
Datasheet Datasheet
Reactivity Human
Source Escherichia coli (E. coli)
Validations
  • (1)
Cat. No. ABIN3077937
Quantity 1 mg
Datasheet Datasheet
Reactivity Mouse
Source Escherichia coli (E. coli)
Validations
  • (1)
Cat. No. ABIN3123292
Quantity 1 mg
Datasheet Datasheet

Synonyms and alternative names related to CLCN1

chloride voltage-gated channel 1 (CLCN1), chloride channel, voltage-sensitive 1a (clcn1a), chloride channel protein 1 (LOC100550479), chloride channel protein 1 (LOC703944), chloride channel, voltage-sensitive 1 (Clcn1), chloride voltage-gated channel 1 (Clcn1), adr, Clc-1, Clc1, CLC1, CLCN1, mto, myotonia, nmf355, si:dkey-14o18.5, SMCC, SMCC1

Protein level used designations for CLCN1

  • chloride channel 1, skeletal muscle
  • chloride channel 1, skeletal muscle (Thomsen disease, autosomal dominant)
  • chloride channel protein 1-like
  • similar to chloride channel 1, skeletal muscle (Thomsen disease, autosomal dominant)
  • arrested development of righting response
  • chloride channel protein 1
  • chloride channel protein, skeletal muscle
  • chloride channel 1, skeletal muscle C-type
  • clC-1
  • skeletal muscle chloride channel 1
  • skeletal muscle chloride channel ClC-1
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