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HADHA antibody (Middle Region)
HADHA
Reactivity: Human
WB
Host: Rabbit
Polyclonal
unconjugated
Product Details anti-HADHA Antibody
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Target
See all HADHA Antibodies
HADHA
(Hydroxyacyl-Coenzyme A Dehydrogenase/3-Ketoacyl-Coenzyme A Thiolase/enoyl-Coenzyme A Hydratase (Trifunctional Protein), alpha Subunit (HADHA))
Binding Specificity
All epitopes for HADHA antibodies
Middle Region
Reactivity
All reactivities for HADHA antibodies
Human
Host
All hosts for HADHA antibodies
Rabbit
Clonality
All clonalities for HADHA antibodies
Polyclonal
Conjugate
All conjugates for HADHA antibodies
This HADHA antibody is un-conjugated
Application
All applications for HADHA antibodies
Western Blotting (WB)
Sequence
IYQEGVKRKD LNSDMDSILA SLKLPPKSEV SSDEDIQFRL VTRFVNEAVM
Purification
Affinity purified
Immunogen
The immunogen is a synthetic peptide directed towards the middle region of human HADHA
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Alternatives
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Application Details
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Application Notes
Optimal working dilution should be determined by the investigator.
Restrictions
For Research Use only
Handling
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Format
Liquid
Buffer
Liquid. Purified antibody supplied in 1x PBS buffer with 0.09 % (w/v) sodium azide and 2 % sucrose.
Preservative
Sodium azide
Precaution of Use
This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
Storage
-20 °C
Storage Comment
For short term use, store at 2-8°C up to 1 week. For long term storage, store at -20°C in small aliquots to prevent freeze-thaw cycles.
Target Details for HADHA
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Target
HADHA
(Hydroxyacyl-Coenzyme A Dehydrogenase/3-Ketoacyl-Coenzyme A Thiolase/enoyl-Coenzyme A Hydratase (Trifunctional Protein), alpha Subunit (HADHA))
Alternative Name
HADHA (HADHA Products )
Synonyms
cb1055 antibody, hadha antibody, im:7136067 antibody, wu:fa14c08 antibody, ECHA antibody, GBP antibody, HADH antibody, LCEH antibody, LCHAD antibody, MTPA antibody, TP-ALPHA antibody, RGD1560655 antibody, C77020 antibody, Mtpa antibody, hydroxyacyl-CoA dehydrogenase trifunctional multienzyme complex subunit alpha antibody, hydroxyacyl-CoA dehydrogenase/3-ketoacyl-CoA thiolase/enoyl-CoA hydratase (trifunctional protein), alpha subunit antibody, hydroxyacyl-CoA dehydrogenase trifunctional multienzyme complex subunit alpha S homeolog antibody, hydroxyacyl-CoA dehydrogenase trifunctional multienzyme complex subunit alpha a antibody, hydroxyacyl-Coenzyme A dehydrogenase/3-ketoacyl-Coenzyme A thiolase/enoyl-Coenzyme A hydratase (trifunctional protein), alpha subunit antibody, HADHA antibody, hadha antibody, hadha.S antibody, hadhaa antibody, Hadha antibody
Background
This gene encodes the alpha subunit of the mitochondrial trifunctional protein, which catalyzes the last three steps of mitochondrial beta-oxidation of long chain fatty acids. The mitochondrial membrane-bound heterocomplex is composed of four alpha and four beta subunits, with the alpha subunit catalyzing the 3-hydroxyacyl-CoA dehydrogenase and enoyl-CoA hydratase activities. Mutations in this gene result in trifunctional protein deficiency or LCHAD deficiency. The genes of the alpha and beta subunits of the mitochondrial trifunctional protein are located adjacent to each other in the human genome in a head-to-head orientation. Alias Symbols: GBP, ECHA, HADH, LCEH, MTPA, LCHAD, TP-ALPHA Protein Size: 763
Gene ID
3030
NCBI Accession
NM_000182 , NP_000173
UniProt
P40939
Pathways
Monocarboxylic Acid Catabolic Process
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