GNS antibody (AA 293-552)
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- Target See all GNS Antibodies
- GNS (Glucosamine (N-Acetyl)-6-Sulfatase (GNS))
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Binding Specificity
- AA 293-552
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Reactivity
- Human
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Host
- Rabbit
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Clonality
- Polyclonal
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Conjugate
- This GNS antibody is un-conjugated
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Application
- Western Blotting (WB)
- Sequence
- WQTLLSVDDL VEKLVKRLEF TGELNNTYIF YTSDNGYHTG QFSLPIDKRQ LYEFDIKVPL LVRGPGIKPN QTSKMLVANI DLGPTILDIA GYDLNKTQMD GMSLLPILRG ASNLTWRSDV LVEYQGEGRN VTDPTCPSLS PGVSQCFPDC VCEDAYNNTY ACVRTMSALW NLQYCEFDDQ EVFVEVYNLT ADPDQITNIA KTIDPELLGK MNYRLMMLQS CSGPTCRTPG VFDPGYRFDP RLMFSNRGSV RTRRFSKHLL
- Cross-Reactivity
- Human, Mouse, Rat
- Characteristics
- Polyclonal Antibodies
- Purification
- Affinity purification
- Immunogen
- Recombinant fusion protein containing a sequence corresponding to amino acids 293-552 of human GNS (NP_002067.1).
- Isotype
- IgG
- Top Product
- Discover our top product GNS Primary Antibody
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- Application Notes
- WB,1:500 - 1:2000
- Comment
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HIGH QUALITY
- Restrictions
- For Research Use only
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- Format
- Liquid
- Buffer
- PBS with 0.02 % sodium azide,50 % glycerol, pH 7.3.
- Preservative
- Sodium azide
- Precaution of Use
- This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
- Storage
- -20 °C
- Storage Comment
- Store at -20°C. Avoid freeze / thaw cycles.
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- Target
- GNS (Glucosamine (N-Acetyl)-6-Sulfatase (GNS))
- Alternative Name
- GNS (GNS Products)
- Synonyms
- G6S antibody, 2610016K11Rik antibody, AU042285 antibody, C87209 antibody, N28088 antibody, NV14559 antibody, N-acetylglucosamine-6-sulfatase antibody, zgc:114066 antibody, gns antibody, wu:fi20h10 antibody, zgc:55370 antibody, glucosamine (N-acetyl)-6-sulfatase antibody, glucosamine (N-acetyl)-6-sulfatase S homeolog antibody, glucosamine (N-acetyl)-6-sulfatase a antibody, N-acetylglucosamine-6-sulfatase antibody, glucosamine (N-acetyl)-6-sulfatase (Sanfilippo disease IIID), b antibody, GNS antibody, Gns antibody, gns.S antibody, gns antibody, gnsa antibody, CpipJ_CPIJ000745 antibody, Sros_7372 antibody, VDBG_04409 antibody, Halhy_3165 antibody, gnsb antibody
- Background
- The product of this gene is a lysosomal enzyme found in all cells. It is involved in the catabolism of heparin, heparan sulphate, and keratan sulphate. Deficiency of this enzyme results in the accumulation of undegraded substrate and the lysosomal storage disorder mucopolysaccharidosis type IIID (Sanfilippo D syndrome). Mucopolysaccharidosis type IIID is the least common of the four subtypes of Sanfilippo syndrome.,GNS,G6S,Cancer,Signal Transduction,Cell Biology & Developmental Biology,Ubiquitin,Endocrine & Metabolism,Amino acid metabolism,GNS
- Molecular Weight
- 59 kDa/62 kDa
- Gene ID
- 2799
- UniProt
- P15586
- Pathways
- Glycosaminoglycan Metabolic Process
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