HADHA antibody
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- Target See all HADHA Antibodies
- HADHA (Hydroxyacyl-Coenzyme A Dehydrogenase/3-Ketoacyl-Coenzyme A Thiolase/enoyl-Coenzyme A Hydratase (Trifunctional Protein), alpha Subunit (HADHA))
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Reactivity
- Human, Mouse
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Host
- Rabbit
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Clonality
- Polyclonal
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Conjugate
- This HADHA antibody is un-conjugated
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Application
- Western Blotting (WB), Immunofluorescence (IF)
- Purification
- Affinity purification
- Immunogen
- Recombinant protein of human HADHA
- Isotype
- IgG
- Top Product
- Discover our top product HADHA Primary Antibody
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- Application Notes
- WB 1:500 - 1:2000 IF 1:50 - 1:200
- Restrictions
- For Research Use only
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- Concentration
- 1 mg/mL
- Buffer
- Buffer: PBS with 0.02 % sodium azide, 50 % glycerol, pH 7.3.
- Preservative
- Sodium azide
- Precaution of Use
- This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
- Storage
- -20 °C
- Storage Comment
- Store at -20°C. Avoid freeze / thaw cycles.
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- Target
- HADHA (Hydroxyacyl-Coenzyme A Dehydrogenase/3-Ketoacyl-Coenzyme A Thiolase/enoyl-Coenzyme A Hydratase (Trifunctional Protein), alpha Subunit (HADHA))
- Alternative Name
- HADHA (HADHA Products)
- Synonyms
- cb1055 antibody, hadha antibody, im:7136067 antibody, wu:fa14c08 antibody, ECHA antibody, GBP antibody, HADH antibody, LCEH antibody, LCHAD antibody, MTPA antibody, TP-ALPHA antibody, RGD1560655 antibody, C77020 antibody, Mtpa antibody, hydroxyacyl-CoA dehydrogenase trifunctional multienzyme complex subunit alpha antibody, hydroxyacyl-CoA dehydrogenase/3-ketoacyl-CoA thiolase/enoyl-CoA hydratase (trifunctional protein), alpha subunit antibody, hydroxyacyl-CoA dehydrogenase trifunctional multienzyme complex subunit alpha S homeolog antibody, hydroxyacyl-CoA dehydrogenase trifunctional multienzyme complex subunit alpha a antibody, hydroxyacyl-Coenzyme A dehydrogenase/3-ketoacyl-Coenzyme A thiolase/enoyl-Coenzyme A hydratase (trifunctional protein), alpha subunit antibody, HADHA antibody, hadha antibody, hadha.S antibody, hadhaa antibody, Hadha antibody
- Background
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Synonyms: 3 ketoacyl Coenzyme A (CoA) thiolase alpha subunit,3 oxoacyl CoA thiolase,78 kDa gastrin binding protein,78 kDa gastrin-binding protein,ECHA,ECHA,GBP,HADH,HADHA,Hydroxyacyl Coenzyme A dehydrogenase/3 ketoacyl Coenzyme A thiolase/enoyl Coenzyme A hydratase (trifunctional protein) alpha subunit,LCEH,LCHAD,Long chain 3-hydroxyacyl-CoA dehydrogenase,Mitochondrial long chain 2 enoyl Coenzyme A (CoA) hydratase alpha subunit,Mitochondrial long chain L 3 hydroxyacyl Coenzyme A dehydrogenase alpha subunit,Mitochondrial trifunctional enzyme alpha subunit,Mitochondrial trifunctional protein alpha subunit,MTPA,Thiolase/enoyl Coenzyme A hydratase (trifunctional protein) alpha subunit,TP ALPHA,TP-alpha,Trifunctional enzyme subunit alpha mitochondrial precursor
Background: This gene encodes the alpha subunit of the mitochondrial trifunctional protein, which catalyzes the last three steps of mitochondrial beta-oxidation of long chain fatty acids. The mitochondrial membrane-bound heterocomplex is composed of four alpha and four beta subunits, with the alpha subunit catalyzing the 3-hydroxyacyl-CoA dehydrogenase and enoyl-CoA hydratase activities. Mutations in this gene result in trifunctional protein deficiency or LCHAD deficiency. The genes of the alpha and beta subunits of the mitochondrial trifunctional protein are located adjacent to each other in the human genome in a head-to-head orientation.
- Molecular Weight
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Observed_MW: 82kDa
Calculated_MW: 28kDa/83kDa
- Gene ID
- 3030
- UniProt
- P40939
- Pathways
- Monocarboxylic Acid Catabolic Process
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