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D2HGDH Products

(D-2-Hydroxyglutarate Dehydrogenase (D2HGDH))
This gene encodes D-2hydroxyglutarate dehydrogenase, a mitochondrial enzyme belonging to the FAD-binding oxidoreductase/transferase type 4 family. This enzyme, which is most active in liver and kidney but also active in heart and brain, converts D-2-hydroxyglutarate to 2-ketoglutarate. Mutations in this gene are present in D-2-hydroxyglutaric aciduria, a rare recessive neurometabolic disorder causing developmental delay, epilepsy, hypotonia, and dysmorphic features. [provided by RefSeq, Jul 2008].

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Featured D2HGDH Categories

D2HGDH Antibodies

High quality antibodies with extensive validation data.

D2HGDH ELISA Kits

Reliable ELISA kits for a wide range of species.

D2HGDH Proteins

Proteins for various applications incl. WB, ELISA, IF etc.

Recommended D2HGDH Antibodies

Product
Reactivity
Application
Validations
Cat. No.
Quantity
Datasheet
Reactivity Human
Application WB, IHC, IP, ICC
Validations
  • (10)
Cat. No. ABIN7442156
Quantity 100 μL
Datasheet Datasheet
Reactivity Human, Mouse, Rat
Application WB, IHC
Validations
  • (2)
Cat. No. ABIN6261211
Quantity 100 μL
Datasheet Datasheet
Reactivity Human
Application ELISA, WB
Validations
  • (1)
Cat. No. ABIN7149434
Quantity 100 μg
Datasheet Datasheet

Recommended D2HGDH ELISA Kits

Product
Reactivity
Analytical Method
Validations
Cat. No.
Quantity
Datasheet
Reactivity Human
Analytical Method Quantitative Sandwich ELISA
Validations
  • (1)
  • (1)
Cat. No. ABIN6955278
Quantity 96 tests
Datasheet Datasheet

Recommended D2HGDH Proteins

Product
Reactivity
Source
Validations
Cat. No.
Quantity
Datasheet
Reactivity Human
Source Insect Cells
Validations
  • (1)
Cat. No. ABIN3078575
Quantity 1 mg
Datasheet Datasheet
Reactivity Mouse
Source Insect Cells
Validations
  • (1)
Cat. No. ABIN3126099
Quantity 1 mg
Datasheet Datasheet
Reactivity Human
Source Escherichia coli (E. coli)
Validations
Cat. No. ABIN7414291
Quantity 100 μg
Datasheet Datasheet

Latest Publications for our D2HGDH products

Gelman, Mahieu, Cho, Llufrio, Wencewicz, Patti: "Evidence that 2-hydroxyglutarate is not readily metabolized in colorectal carcinoma cells." in: Cancer & metabolism, Vol. 3, pp. 13, (2015) (PubMed).

Synonyms and alternative names related to D2HGDH

D-2-hydroxyglutarate dehydrogenase (D2hgdh), D-2-hydroxyglutarate dehydrogenase (D2HGDH), D-2-hydroxyglutarate dehydrogenase (d2hgdh), AA408776, AA408778, AI325464, D2HGD, RGD1307976, zgc:158661

Protein level used designations for D2HGDH

  • D-2-hydroxyglutarate dehydrogenase, mitochondrial
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